Abstract
Ebstein anomaly and tricuspid valve dysplasia (EA/TVD) are rare congenital tricuspid valve
malformations that carry among the highest mortality of all congenital heart disease
diagnosed in utero. Despite the high mortality associated with severe EA/TVD in the fetus, it
has only been studied retrospectively. By prospectively enrolling a cohort across multiple
centers, many questions may be answered in the perinatal period and beyond. The registry will
allow us to understand perinatal and postnatal decision-making in this complex group of
patients across centers.
